The weeping heart, the choked lung, the blinded eye, and the crying femur: A saga of juvenile dermatomyositis Hegde A, Acharya S, Shankar S, Kumar A, Kovilapu UB, - J Indian Prosthodont Soc

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The weeping heart, the choked lung, the blinded eye, and the crying femur: A saga of juvenile dermatomyositis Arun Hegde¹, Suchi Acharya², Subramanian Shankar³, Abhishek Kumar⁴, Uday Bhanu Kovilapu⁵ ¹ Department of Rheumatology, Command Hospital (Southern Command), Pune, Maharashtra, India ² Department of Pediatrics, AFMC, Pune, Maharashtra, India ³ Department of Rheumatology, Army hospital (Research and Referral), Delhi cantt, Air Cmde AFMS (P&T), O/o DGAFMS, New Delhi, India ⁴ Department of Rheumatology, Command Hospital (Eastern Command), Kolkata, West Bengal, India ⁵ Department of Radiodiagnosis, AFMC, Pune, Maharashtra, India Correspondence Address: Suchi Acharya, Department of Pediatrics, AFMC, Wanowrie, Pune - 411 040, Maharashtra India Source of Support: None, Conflict of Interest: None DOI: 10.4103/injr.injr_51_21

Juvenile dermatomyositis (JDM) is the most common inflammatory myositis in children that primarily involves the skeletal muscles and skin. However, it can manifest with a diverse range of clinical features across multiple organ systems. JDM vasculopathy causing optic neuritis and medullary bone infarcts in children are rare manifestations of JDM and have been seldom reported in literature. Similarly, cardiovascular manifestations in the form of refractory myocarditis leading to congestive cardiac failure during the early course of the disease have also been rare findings. Early diagnosis and aggressive management of such complications using biological disease-modifying synthetic antirheumatic drugs has significantly reduced the mortality and morbidity associated with JDM. Herein, we report a mini case series of three patients with JDM who presented with these rare systemic manifestations and achieved favorable outcomes while being managed using the Childhood Arthritis and Research Alliance-Treatment Protocols.

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    -  Hegde A
    -  Acharya S
    -  Shankar S
    -  Kumar A
    -  Kovilapu UB

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